Skip to main content

Table 2 Clinical data of the patients completed both modified Marshall`s and Eurofever/PRINTO criteria

From: Unravelling the clinical heterogeneity of undefined recurrent fever over time in the European registries on Autoinflammation

 

JIR-cohort (n = 122)

Eurofever (n = 226)

AID-net (n = 40)

Age of diagnose years*

3.91 (0.81 – 4.99)

3.4 (1.2 – 4.83)

3.7 (0.75—5)

Boys/girls

68/54

117/109

21/19

Patients < 18 y.o. when diagnosed

122 (100%)

226 (100%)

40 (100%)

Fever > 38 C

122 (100%)

226 (100%)

40 (100%)

Duration of the episode, daysa

4 (3—6)

3 (3—6)

3 (3—6)

Pharyngitis

113 (92.6%)

173 (76.5%)

31 (77.5%)

Cervical adenopathy

92 (75.4%)

159 (70.3%)

34 (85%)

Aphthous stomatitis

49 (40.1%)

106 (46.9%)

21 (52.5%)

Others

 Headache

22 (18%)

54 (23.9%)

15 (37.5%)

 Diarrhoea

0

0

0

 Rash

0

0

0

 Arthritis

0

0

0

  1. Patients with PFAPA selected from 3 registries and completed both – modified Marshalls and Eurofever/PRINTO criteria presented in current table, reflecting demography and relevant clinical information. aMedian, q1-q3