Exploring the clinical profiles and management of juvenile dermatomyositis in Africa: a survey of African rheumatology care providers

Table 1 Clinical outcomes in children with juvenile dermatomyositis in Africa among survey respondents (n = 20)

Country (Number of Respondents)	Total Patients (n = 216)^*	Clinically Inactive Disease^†	Remission^‡	Calcinosis	Interstitial Lung Disease	Deaths
Northern Africa (12; 60%)
Egypt (6]	68^*	28	13	36	5	2
Libya [3]	55^*	18⁺	39⁺	12	5⁺	3
Morocco [1]	19	6 (31.6%)	4 (21.1%)	7 (36.8%)	6 (31.6%)	0 (0%)
Tunisia [2]	3^*	6	6	0	4	0⁺
Eastern Africa (3; 15%)
Kenya [2]	42	15 (35.7%)	12 (28.6%)	13 (31.0%)	8 (19.0%)	6 (14.3%)
Zambia [1]	7	5 (71.4%)	0 (0%)	3 (42.9%)	1 (14.3%)	2 (28.6%)
Central Africa (3; 15%)
Cameroon [2]^**	11	6 (54.5%)	5 (45.5%)	3 (27.3%)	2 (18.2%)	0 (0%)
Democratic Republic of the Congo [1]^**	3	3 (100%)	1 (33.3%)	3 (100%)	0 (0%)	⁺
Western Africa (1; 5%)
Nigeria [1]	4	2 (50.0%)	1 (25.0%)	0 (0%)	1 (25.0%)	0 (0%)
Southern Africa (1; 5%)
South Africa [1]	4	1 (25.0%)	1 (25.0%)	2 (50.0%)	0 (0%)	0 (0%)

Number of patients reported as n; (%) also reported when total patients known
*At least 1 respondent unsure of total number of patients, therefore number provided is an underestimation and percentages were unable to be calculated; Egypt = 3 of 6 respondents unsure about prior patients, Libya = 1 of 3 respondents unsure about total current and total prior patients, Tunisia = 2 of 2 respondents unsure about total current patients and 1 of 2 unsure about prior patients.
† Defined as lack of evidence of myositis disease activity as assessed by global and extra-muscular assessments, stable muscle strength and function, and normal muscle enzyme levels, as per the International Myositis Assessment & Clinical Studies (IMACS) criteria for lack of evidence of active myositis
‡ Defined according to the IMACS 2005 definition: clinically inactive disease while not receiving any drug therapy for a 6-month continuous period
**Respondents answered questions only about current, not prior, patients (Cameroon = 1 respondent, Democratic Republic of Congo = 1 respondent)
+ Response missing from 1 respondent

ISSN: 1546-0096