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Table 1 Published case reports and series of pediatric patients with protracted febrile myalgia syndrome

From: Protracted febrile myalgia syndrome in children with familial Mediterranean fever – systematic review and a case report

Author

Year

Journal

Authors from

Number of patients

Primary manifestation

Afebrile course

Myalgia

Abdominal pain

Rash

Corticosteroids effective

Anakinra effecitve

Majeed et al

2000

Semin Arthritis Rheum

Jordan

7

3

0

7

4

1

3

-

Tekin et al

2000

Acta Paediatr

Turkey

9

0

0

9

6

8

8

-

Ertekin et al

2005

Rheum Int

Turkey

2

2

0

2

1

0

2

-

Soylu et al

2006

J Clin Rheumatol

Turkey

6

5

0

6

5

2

6

-

Bircan et al

2008

J Clin Rheumatol

Turkey

6

1

0

6

5

0

6

-

Soylu et al

2008

Semin Arthritis Rheum

Turkey

1

1

0

1

0

0

1

-

Duru et al

2010

Ped international

Turkey

2

0

0

2

1

1

2

-

Senel et al

2010

Mod Rheumatol

Turkey

1

0

0

1

0

1

1

-

Bircan et al

2010

Semin Arthritis Rheum

Turkey

1

0

0

1

0

1

0

-

Demir et al

2012

Pediatr diab

Turkey

1

0

1

1

1

0

1

-

Oguz et al

2016

Indian J Pediatr

Turkey

1

1

1

1

0

0

1

-

Rom et al

2017

Semin Arthritis Rheum

Israel

8

4

0

8

8

0

8

-

Yildirim et al

2019

Rheum Int

Turkey

5

1

0

5

5

3

2

2

Cakan et al

2020

North Clin Istanb

Turkey

1

1

0

1

1

0

0

1

Ling et al

2021

J Clin Rheumatol

Israel

1

0

1

1

0

0

1

-

Öztürk et al

2021

Rheum Int

Turkey

6

6

2

6

2

1

4

-

Aviran et al

2022

Orphanet J Rare Dis

Israel

5

5

0

5

2

0

2

-

Aydin

2023

Mod Rheumato

Turkey

14

11

3

14

9

1

11

2

Hospach (present case)

2024

 

Germany

1

1

0

1

1

1

-

-

Sum (%)

   

78

42 (54)

8 (10)

78 (100)

51 (65)

20 (26)

59/77 (77)

5/5 (100)

  1. Abbreviation: NSAID nonsteroidal anti-inflammatory drugs